Ichthyosis
Other types of inherited ichthyosis
Source: NHS
In this topic (7)
Other inherited forms ofichthyosis are very rare and include:
- X-linked ichthyosis only affects males and includes general scaling, particularly over the limbs and trunk (torso)
- congenital ichthyosiform erythroderma
- harlequin ichthyosis thisis extremely rare, but the scaling is severe and requires intensive care at birth
- syndromes that include ichthyosis such as Netherton's syndrome or Sjgren-Larsson syndrome
Congenital ichthyosiform erythroderma
Ichthyosis may develop if a baby is born with a shiny yellow membrane (collodion membrane)that sheds within the first week of life.
Once the membrane has shed, one of the following types of ichthyosis can develop:
- non-bullous ichthyosiform erythroderma inflamedscaly skin that affects the entire skin surface
- bullousichthyosiform erythroderma inflamed scaly skin with fluid-filled blisters that may become infected andproduce a foul-smelling skin odour
- lamellar ichthyosis where the skin isn't as red, but the scales are larger and tighter to the skin
Insevere cases ofcongenital ichthyosiform erythrodermaa child may also have drooping lower eyelids (ectropion) , mild hair loss and tight skin on the fingers.
Articles for Ichthyosis
Acquired ichthyosis
Acquired ichthyosis tends to develop in adulthood and isn't inherited. It's usually associated with another condition, such as: an underactive thyroid kidney disease sarcoidosis a rare condition
Ichthyosis vulgaris
Ichthyosis vulgaris is the most common type of inheritedichthyosis, affecting1 in 250-1,000 people. Signs and symptomsinclude: skin may appear normal at birth skin gradually becomes dry, rough and
Introduction
Find out about ichthyosis, a condition that causes widespread and persistent thick, dry, "fish-scale" skin.
Other types of inherited ichthyosis
Other inherited forms ofichthyosis are very rare and include: X-linked ichthyosis only affects males and includes general scaling, particularly over the limbs and trunk (torso) congenital ichthyo
Outlook
People with mild ichthyosis have a normal lifespan. However,the most severe inherited types can be life threatening. If you have inherited ichthyosis, you'll have it for life. Acquired ichthyosis may
Treating ichthyosis
There's no cure for ichthyosis, butmoisturising and exfoliating the skin daily can help prevent dryness, scaling and the build-up of skin cells. Skincare Your skin specialist (dermatologist) will be
What causesichthyosis
Most people with ichthyosis have inherited a particular faulty gene from their parent. The signs and symptoms of inherited ichthyosis appear at birth or within the first year of life. The faulty gene